Journal of Stroke & Cerebrovascular Diseases
Volume 19, Issue 1 , Pages 75-76, January 2010

Acute Headache Followed by Focal Neuropsychological Impairment in Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL)

  • François Ducray, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • Inserm U842, Lyon, France
    • Corresponding Author InformationAddress correspondence to François Ducray, MD, Department of Neurology B, Cerebrovascular Unit, Universite Lyon 1, 59 Boulevard Pinal 69394 Lyon Cedex 03 Lyon, France.
    • ,
  • Thomas Ritzenthaler, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • ,
  • Tae Hee Cho, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • Department of Radiology, Centre Hospitalier Lyon Sud, Lyon, France
    • ,
  • Amandine Bruyas, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • ,
  • François Cotton, MD, PhD

      Affiliations

    • Creatis CNRS UMR 5520-Inserm U 630, Lyon, France
    • Department of Radiology, Centre Hospitalier Lyon Sud, Lyon, France
    • ,
  • Stéphanie Cartalat-Carel, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • ,
  • Jérôme Honnorat, MD, PhD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • Inserm U842, Lyon, France
    • ,
  • Norbert Nighoghossian, MD

      Affiliations

    • Department of Neurology B, Cerebrovascular Unit, Université Lyon 1, Lyon, France
    • Department of Radiology, Centre Hospitalier Lyon Sud, Lyon, France

Received 14 February 2009; accepted 6 March 2009.

Occasionally, patients with Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL) present atypical features such as confusion, coma, or nonconvulsive status epilepticus. Acute focal neuropsychological syndrome revealing the disease has been poorly documented. We report the atypical presentation of two patients in whom CADASIL was revealed by an episode of headache followed by focal neuropsychological impairment.

Key Words: CADASIL, headache, neuropsychology

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PII: S1052-3057(09)00046-9

doi:10.1016/j.jstrokecerebrovasdis.2009.03.001

Journal of Stroke & Cerebrovascular Diseases
Volume 19, Issue 1 , Pages 75-76, January 2010

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